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DL-3-AMINOISOBUTYRIC ACID
CAS No. 144-90-1
DL-3-AMINOISOBUTYRIC ACID ( 3-Amino-2-methylpropanoic acid;α-Methyl-β-alanine )
Catalog No. M19753 CAS No. 144-90-1
beta-aminoisobutyric acid is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6) the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.
Purity : >98% (HPLC)
COA
Datasheet
HNMR
HPLC
MSDS
Handing Instructions
| Size | Price / USD | Stock | Quantity |
| 100MG | 37 | In Stock |
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| 200MG | Get Quote | In Stock |
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| 500MG | Get Quote | In Stock |
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| 1G | Get Quote | In Stock |
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Biological Information
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Product NameDL-3-AMINOISOBUTYRIC ACID
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NoteResearch use only not for human use.
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Brief Descriptionbeta-aminoisobutyric acid is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6) the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.
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Descriptionbeta-aminoisobutyric acid is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6) the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.
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Synonyms3-Amino-2-methylpropanoic acid;α-Methyl-β-alanine
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PathwayProteasome/Ubiquitin
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TargetEndogenous Metabolite
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RecptorHuman Endogenous Metabolite
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Research Area——
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Indication——
Chemical Information
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CAS Number144-90-1
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Formula Weight103.12
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Molecular FormulaC4H9NO2
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Purity>98% (HPLC)
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SolubilityDMSO:10 mM
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SMILESCC(CN)C(O)=O
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Chemical Name——
Shipping & Storage Information
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Storage(-20℃)
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ShippingWith Ice Pack
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Stability≥ 2 years
Reference
1.Kuilenburg A B P V Meinsma R Beke E et al. beta-Ureidopropionase deficiency: an inborn error of pyrimidine degradation associated with neurological abnormalities.[J]. Human Molecular Genetics 2004 13(22):2793-2801.
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